Ìåíþ

Ãëàâíàÿ
Ñëó÷àéíàÿ ñòàòüÿ
Íàñòðîéêè
GP1BA
Ìàòåðèàë èç https://ru.wikipedia.org

Òðîìáîöèòàðíûé ãëèêîïðîòåèí Ib, àëüôà öåïü (àíãë. Glycoprotein Ib; GP1BA; CD42b) — ìåìáðàííûé áåëîê, ïðîäóêò ãåíà ÷åëîâåêà GP1BA.[5]

Ñîäåðæàíèå

Ôóíêöèè

Ãëèêîïðîòåèí Ib (GP Ib) ÿâëÿåòñÿ òðîìáîöèòàðíûì ìåìáðàííûì ãëèêîïðîòåèíîì, ãåòåðîäèìåðîì. Ïîëíûé êîìïëåêñ âêëþ÷àåò ñîáñòâåííî ãåòåðîäèìåð GP Ib èç äâóõ ïîëèïåïòèäíûõ öåïåé: àëüôà-öåïè GP1BA è áåòà-öåïè GP1BB, ñîåäèí¸ííûõ äèñóëüôèäíîé ñâÿçüþ, à òàêæå íåêîâàëåíòíî-àññîöèèðîâàííûå ãëèêîïðîòèíû IX è V. Êîìïëåêñ ôóíêöèîíèðóåò êàê ðåöåïòîð ôàêòîðà ôîí Âèëëåáðàíäà[5]. Ìóòàöèè GP1BA ïðèâîäÿò ê ñèíäðîìó Áåðíàðà-Ñóëüå è áîëåçíè ôîí Âèëëåáðàíäà.

Âçàèìîäåéñòâèÿ

GP1BA âçàèìîäåéñòâóåò ñ ðåãóëÿòîðíûì áåëêîì YWHAZ èç ñåìåéñòâà 14-3-3[6][7][8] è àêòèí-ñâÿçûâàþùèì áåëêîì FLNB.[9]

Ïðèìå÷àíèÿ
  1. 1 2 3 GRCh38: Ensembl release 89: ENSG00000185245 - Ensembl, May 2017
  2. 1 2 3 GRCm38: Ensembl release 89: ENSMUSG00000050675 - Ensembl, May 2017
  3. Ññûëêà íà ïóáëèêàöèþ ÷åëîâåêà íà PubMed: Íàöèîíàëüíûé öåíòð áèîòåõíîëîãè÷åñêîé èíôîðìàöèè, Íàöèîíàëüíàÿ ìåäèöèíñêàÿ áèáëèîòåêà ÑØÀ.
  4. Ññûëêà íà ïóáëèêàöèþ ìûøè íà PubMed: Íàöèîíàëüíûé öåíòð áèîòåõíîëîãè÷åñêîé èíôîðìàöèè, Íàöèîíàëüíàÿ ìåäèöèíñêàÿ áèáëèîòåêà ÑØÀ.
  5. 1 2 Entrez Gene: GP1BA glycoprotein Ib (platelet), alpha polypeptide.
  6. Calverley, Kavanagh, Roth, 1998.
  7. Du, Fox, Pei, 1996.
  8. Feng, Christodoulides, Resndiz, 2000.
  9. Takafuta, Wu, Murphy, Shapiro, 1998.


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